WHAT IS FABRY DISEASE
Fabry
Disease is an hereditary disorder causing the partial or total deficit of a
lysosomal enzyme (alpha-galactosidase A or alpha-GAL A). Due to this enzyme
deficit, some substances are no longer cleared from the body and remain within
the cells.
The
progressive storage of these substances starts even before birth, in the mother's
stomach, and triggers almost all the problems related to Fabry disease.